Abstract: Twenty-seven patients with renal artery fibtromuscular dysplasia（FMD） were investiged,age 25±7 years（ranging from 2 months to 12 years）.Hypertension was persistent elevated in 24 patients（88.9％）.Significant blood pressure fluctuation was seen in 3 cases （11.1％）. 7 patients had a bruit in the abdomen,50％ patients with hypokalemia,2 cases with mild cardiomegaly and 2 cases with mild impairment of renal function.All patients had normal angiography in the thoracic aorta and abdominal aorta.The lesion involved only the right renal artery in 55.6％,and involved both the right and left renal arteies in 14.8％.The lesion was often located in the middle or distal part of the renal artery.9 patients showed a string-of-beads stenosis.These findings suggested that FMD seems to be a common cause of renovascular hypertension（RVH）in youing women, with the right renal artery more being commonly involved.Cardiomegaly and impaired renal function were rare in FMD.